Extra Hepatic Portal Vein Obstruction with Solitary Left Kidney: A Case Report

Pabitra Adhikari; Nirajan Regmi; Akash Chitrakar; Bikal Ghimire; Yogendra P. Singh

Pabitra Adhikari Department of GI and General surgery, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Nirajan Regmi Department of GI and General surgery, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Akash Chitrakar Department of GI and General surgery, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Bikal Ghimire Department of GI and General surgery, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Yogendra P. Singh Department of GI and General surgery, Institute of Medicine, Maharajgunj, Kathmandu, Nepal

Abstract

DOI: https://doi.org/10.31729/jnma.4214 EHPVO in individual with solitary left kidney is rare occurance. Though there is no etiological association between EHPVO and solitary left kidney but the solitary left kidney decides the modality of treatment. Eighteen year lady referred to our institute with menorrhagia for 5 years and ultrasonography finding of splenomegaly and atretic right kidney. Investigations revealed Extra Hepatic Portal Vein Obstruction with multiple cavernoma formation with oesophagogastric varices with right renal agenesis. She successfully underwent splenectomy with devascularisation. Patient with EHPVO present mainly with recurrent episodes of variceal bleeding, splenomegaly and hypersplenism. Splenectomy and esophagogastric devascularisation is an effective modality of treatment for patient with EHPVO with solitary kidney.

Keywords: cavernoma; EHPVO; modified Hassab’s operation; unilateral renal agenesis.