Rahar, SChaudhary, A2026-05-282026-05-282012https://hdl.handle.net/20.500.14572/6292S Rahar Senior Resident, Department of Ophthalmology, Safdarjung Hospital and Vardhaman Mahaveer Medical College, New Delhi A Chaudhary Junior Specialist, Department of Paediatrics, Sri Kalyan Hospital, Sikar, RajasthanAbstract: Pantothenate kinase-associated neurodegeneration (PKAN) is a form of neurodegeneration with brain iron accumulation (NBIA), formerly called Hallervorden-Spatz syndrome. PKAN is the first described inborn error of coenzyme A metabolism. PKAN encompasses two clinical subtypes, classic and atypical. We here report an eight year girl diagnosed as classic PKAN. We also review the literature about PKAN.en-USEye of tiger signNBIANeuroregenerationIron AccumulationHallevorden Spatz SyndromeArticle