Devkota, SUpadhyay, S2026-06-042026-06-042010https://hdl.handle.net/20.500.14572/6368S Devkota Medical Officer, Department of Paediatrics, Nepal Medical College and Teaching Hospital, Jorpati, Kathmandu S Upadhyay Lecturer, Department of Paediatrics, Nepal Medical College and Teaching Hospital, Jorpati, KathmanduAbstract: Sturge-Weber syndrome is a neurocutaneous syndrome characterized by port wine stain, congenital glaucoma, and underlying anomalous leptomeningeal venous plexus and the lack of normal cortical venous drainage. It is a congenital but not an inherited disease and it occurs sporadically and is very rare, incidence being approximately 1 on 50000. It occurs with rare exception but occasionally the other members of the family may have hemangiomata of a lesser degree.en-USSturge Weber SyndromeArticle