Amatya, AGurung, GRana, AKhakurel, MPSingh, KP2026-07-012026-07-012006https://hdl.handle.net/20.500.14572/6833A. Amatya Department of Obstetrics and Gynaecology, TU Teaching Hospital G. Gurung Department of Obstetrics and Gynaecology, Department of Surgery, TUTH, Kathmandu A. Rana Department of Obstetrics and Gynaecology, Department of Surgery, TUTH, Kathmandu M.P. Khakurel Department of Obstetrics and Gynaecology, Department of Surgery, TUTH, Kathmandu K.P. Singh Department of Surgery, TUTH, KathmanduAbstract Background: This case concerns a 30 year old unmarried woman who was least bothered by persistent cloacal opening in the perineum from which she had been passing stool, completely being ignorant of normal female anatomy of lower gastrointestinal/urogenital tract and only attended our hospital for combined operative management of cholelithiasis and ovarian dermoid detected by an ultrasound when she presented with 2 years history of abdominal pain. Case report: Laparotomy visualized mullerian anomaly in form of thumb sized uterus without a cervix and unilateral dermoid. Megacolon was also observed as a resultant of cloacal abnormality. Keywords: persistent cloaca, mullerain anomaly, megacolonen-USpersistent cloacamullerain anomalymegacolonMullerain anomaly with a persistent cloaca and an ovarian dermoid- a rare combinationArticle