Maji, BGanguly, NGhosh, A2026-04-232026-04-232014https://hdl.handle.net/20.500.14572/5913B Maji Resident, Institute of Child Health, Park Circus, Kolkata N Ganguly Associate Professor, Institute of Child Health, Park Circus, Kolkata A Ghosh Professor and Director, Institute of Child Health, Park Circus, KolkataAbstract: Unilateral lung agenesis initially misdiagnosed as unilateral massive pleural effusion with collapse of lung, and after several investigations, including ultrasonography or CT scan of thorax, fibre-optic bronchoscopy or bronchography, a final diagnosis of unilateral absence of lung is made. An anomaly scan may also reveal associated renal, cardiac and vertebral defects. Here we report a 7 months old female who presented with respiratory distress since birth and after a thorough investigation, she was found to have this rare association of pulmonary-renal-cardiacvertebral defect.en-USPulmonary agenesisRenal agenesisCardiac anomalyVertebral defectArticle