Simkhada, AnkitaPaudel, RameshSharma, Nisha2025-09-282025-09-282023https://hdl.handle.net/20.500.14572/2423Ankita Simkhada Department of Pathology, Maharajgunj Medical Campus, Maharajgunj, Kathmandu, Nepal https://orcid.org/0000-0002-7123-7641 Ramesh Paudel Department of Pathology, Maharajgunj Medical Campus, Maharajgunj, Kathmandu, Nepal Nisha Sharma Department of Pathology, Maharajgunj Medical Campus, Maharajgunj, Kathmandu, NepalAbstract Congenital mesoblastic nephromas are rare renal tumours that are encountered in paediatric age group. A term female neonate at the end of first week of life presented with bilateral lower limb swelling. On radiological evaluation, ultrasonography revealed an intra-abdominal mass which was managed with radical nephroureterectomy. Histopathological examination confirmed a diagnosis of congenital mesoblastic nephroma of mixed subtype.en-USCase reportsCongenital mesoblastic nephromaKidney neoplasmsNephrectomyOther