Shrestha, RKayastha, Bhaskar MMReema, Aishath2026-05-202026-05-202013https://hdl.handle.net/20.500.14572/6152R Shrestha Clinical Tutor, Department of Dermatology, National academy of Medical Sciences (NAMS), Bir Hospital, Kathmandu Bhaskar MM Kayastha Professor and Head, Department of Dermatology, National academy of Medical Sciences (NAMS), Bir Hospital, Kathmandu Aishath Reema Resident, Department of Dermatology, National academy of Medical Sciences (NAMS), Bir Hospital, KathmanduAbstract: Incontinentia pigmenti is a rare X-linked dominant condition characterized by abnormalities in skin, eyes, teeth, bones and the central nervous system. A seven year old female child presented to the Dermatology Out Patient Department (OPD) of Bir Hospital with vesicles, bullae, verrucous papules and plaques and hypopigmented streaks on the trunk and extremities of six years duration. Based on the clinical findings she was diagnosed as a case of Incontinentia pigmenti.en-USIncontinentia PigmentiArticle