Regmi, NishaShrestha, BibekKarn, VivekRegmi, Pradeep Raj2026-02-082026-02-082025https://hdl.handle.net/20.500.14572/4590Nisha Regmi1, Bibek Shrestha2, Vivek Karn3, Pradeep Raj Regmi4 ¹College of Medical Sciences, Chitwan, Nepal 2Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal 3Department of Pediatrics, Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal 4Department of Radiology, Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, NepalABSTRACT Moyamoya disease is a rare progressive cerebrovascular disorder in Nepal characterized by stenosis or occlusion of cerebral arteries with abnormal collateral vessels, and hemorrhagic presentation in children is extremely uncommon. We report an 8-year-old girl with intraventricular hemorrhage presenting with seizures, vomiting, and decreased consciousness. Imaging revealed characteristic angiographic features of Moyamoya disease. She was managed with external ventricular drainage and supportive treatment, achieving significant recovery. This case highlights the importance of considering Moyamoya disease in pediatric hemorrhagic stroke and underscores the need for early imaging and timely intervention. Keywords: Moyamoya Disease; intraventricular hemorrhage; pediatric strokeen-USMoyamoya Diseaseintraventricular hemorrhagepediatric strokeArticle