M, PradhanKK, MallaSR, ChowdhuryMR, Baral2025-07-152025-07-152004https://hdl.handle.net/20.500.14572/249Schizencephaly is a rare developmental disorder of neuronal migration, characterized by early focal destruction of the germinal matrix and surrounding brain before the cerebral hemispheres are fully formed at 1-5 months of gestation .The lesion is most likely related to multiple aetiologies including genetic, toxic, metabolic, vascular or infectious agents. This case is reported due to its rarity. The prevalence of schizencephaly is very uncommon internationally. Key Words: Schizencephaly, septum pellucidum, septoptic dysplasia.en-USArticle