Publication: Disappearing Bone Disease with Disappearing Spleen!
Date
2009
Authors
Article Type
Case Report
Journal Title
Journal ISSN
ISSN 1990-7974 eISSN 1990-7982
Volume Title
Pages
Pages: 94 - 97
Publisher
Nepal Paediatric Society (JNPS)
Abstract
Abstract:
A 6-year-old girl who reported for pain abdomen was incidentally detected to have multiple osteolytic lesions on X-ray. She was diagnosed as a case of Gorham's disease following confirmation with histopathology and kept on close follow-up. She was admitted again after 2 years for fever and investigations revealed an absent spleen apart from multicentric osteolytic lesions. This is the first case reported of a child with Gorham's disease who has had an auto-splenectomy on follow-up.
Description
BM John
Classified Specialist (Pediatrics), Department of Pediatrics. Command Hospital (Air Force), Bangalore
Daljit Singh
Professor and Head of Department of Pediatrics. Command Hospital (Air Force), Bangalore
Keywords
Gorham's disease (disappearing bone disease), osteolytic lesions, spleen
Identifier
https://doi.org/10.3126/jnps.v29i2.2047