Publication: Recurrent Angioedema: A Case Series of C1 Esterase Inhibitor Deficiency
Date
2025
Journal Title
Journal ISSN
Volume Title
Publisher
Perinatal Society of Nepal (PESON)
Abstract
Abstract:
We report a case series of recurrent angioedema, hereditary and acquired, diagnosed after a long period of time. The first and the second patient presented initially at the age of 13 years and were diagnosed finally at the age of 27 years and 18 years respectively. The third case is reported in an adult and was finally diagnosed as case of acquired angioedema. The patients were managed with danazol and tranexamic acid in absence of standard recommended drugs. The cases highlight the importance of diagnosing cases during childhood and emphasize the need of standard drugs in our scenario.
Description
Upama Paudel
Associate Professor, Department of Dermatology and Venereology, Tribhuvan University Teaching Hospital,Maharajgunj Medical Campus, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Sudip Parajuli
Associate Professor, Department of Dermatology and Venereology, Tribhuvan University Teaching Hospital,Maharajgunj Medical Campus, Institute of Medicine, Maharajgunj, Kathmandu, Nepa
Laxman Chapagain
Resident, Department of Dermatology and Venereology, Tribhuvan University Teaching Hospital,Maharajgunj Medical Campus, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Ashu Sharma
Resident, Department of Dermatology and Venereology, Tribhuvan University Teaching Hospital,Maharajgunj Medical Campus, Institute of Medicine, Maharajgunj, Kathmandu, Nepal
Keywords
Angioedema, Danazol, Ecallantide, Hereditary, Icatibant