Publication:
Hemiconvulsion-Hemiplegia-Epilepsy Syndrome in a Girl Presented with Complex Partial Seizures

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creativeworkseries.issn1812-2027
dc.contributor.authorJoshi, A
dc.contributor.authorShrestha, PS
dc.contributor.authorDangol, S
dc.contributor.authorShrestha, NC
dc.contributor.authorPoudyal, P
dc.contributor.authorShrestha, A
dc.date.accessioned2025-10-30T06:59:46Z
dc.date.available2025-10-30T06:59:46Z
dc.date.issued2017
dc.descriptionJoshi A, Shrestha PS, Dangol S, Shrestha NC, Poudyal P, Shrestha A Department of Pediatrics Dhulikhel Hospital, Kathmandu University Hospital, Dhulikhel, Kavre, Nepal
dc.description.abstractABSTRACT The mechanisms underlying the Hemiconvulsion-Hemiplegia-Epilepsy syndrome remains unclear. The current proposed pathogenic mechanism is a neuronal injury induced by venous thrombosis and/or hypoxia. Children develop hemispheric brain atrophy with contralateral hemiplegia, epilepsy, and a variable degree of cognitive deficit. We report a 33 months old female child a case of hemiconvulsion- hemiplegia-epilepsy syndrome with right hemisphere unilateral brain edema and left sided hemiplegia and aphasia who presented with left upper extremities complex partial seizures with generalization to tonic clonic seizures and developed status epilepticus that posed diagnostic and therapeutic challenges. Progressive atrophy of the right cerebral hemisphere was noted after 3 months of follow up. Hemiconvulsion-Hemiplegia-Epilepsy syndrome should be suspected in a child with unilateral cerebral hemisphere brain edema and hemiplegia with cognitive deficit following status epilepticus to provide patients and families with an accurate prognosis regarding the subsequent development of epilepsy. KEY WORDS Hemiconvulsion-Hemiplegia-Epilepsy syndrome, Hemispheric brain atrophy, Status epilepticus, Unilateral brain edema
dc.identifier.urihttps://hdl.handle.net/20.500.14572/2914
dc.language.isoen_US
dc.publisherKathmandu University
dc.subjectHemiconvulsion-Hemiplegia-Epilepsy syndrome
dc.subjectHemispheric brain atrophy
dc.subjectStatus epilepticus
dc.subjectUnilateral brain edema
dc.titleHemiconvulsion-Hemiplegia-Epilepsy Syndrome in a Girl Presented with Complex Partial Seizures
dc.typeArticle
dspace.entity.typePublication
local.article.typeCase Report
oaire.citation.endPage260
oaire.citation.startPage256
relation.isJournalIssueOfPublicationb101e3f5-50f8-4d60-aa3a-23890244a10c
relation.isJournalIssueOfPublication.latestForDiscoveryb101e3f5-50f8-4d60-aa3a-23890244a10c
relation.isJournalOfPublicationa782b7ff-cf89-4178-ad1c-11ed89cfe1bd

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