Publication:
Thanatophoric Dysplasia

creativeworkseries.issnISSN 1990-7974 eISSN 1990-7982
dc.contributor.authorBadal, Sachendra
dc.contributor.authorRoy, Shuvendu
dc.contributor.authorSingh, Daljit
dc.date.accessioned2026-03-17T11:06:38Z
dc.date.available2026-03-17T11:06:38Z
dc.date.issued2015
dc.descriptionSachendra Badal Graded Specialist (Paediatrics) IMTRAT Military Hospital Shuvendu Roy Senior Advisor (Paediatrics) & Pediatric Neurologist, Army Hospital (R & R), New Delhi 110010 Daljit Singh Air Officer Commanding, 7 Air Force Hospital (Kanpur, UP) and Neonatologist
dc.description.abstractAbstract: Thanatophoric Dysplasia (TD) is a severe skeletal dysplasia that is lethal in the neonatal period. There are two defined TD subtypes which have been classified clinically. The incidence is approximately 1/20,000 to 1/50,000. Type I TD being more frequent than Type II. Most individuals with TD die within the first few hours.This condition has characteristic sonographic features detected antenatally by midgestation, although distinction from other short-limbed dysplasia syndromes may be difficult. We report a case of type I TD with typical clinicoradiological features who succumbed within one hour of life.
dc.identifierhttps://doi.org/10.3126/jnps.v35i3.11946
dc.identifier.urihttps://hdl.handle.net/20.500.14572/5209
dc.language.isoen_US
dc.publisherNepal Paediatric Society (JNPS)
dc.subjectThanatophoric dysplasia
dc.subjectkleeblattschaedel
dc.subjectcloverleaf skull
dc.subjectlethal skeletal dysplasia
dc.titleThanatophoric Dysplasia
dc.typeArticle
dspace.entity.typePublication
local.article.typeCase Report
oaire.citation.endPage306
oaire.citation.startPage304
relation.isJournalIssueOfPublicationddb30430-3a07-48b1-8970-c896f031201d
relation.isJournalIssueOfPublication.latestForDiscoveryddb30430-3a07-48b1-8970-c896f031201d
relation.isJournalOfPublication6f9be05c-05a9-4a3e-a5b5-a19a15ab042c

Files

Original bundle
Now showing 1 - 1 of 1
Loading...
Thumbnail Image
Name:
304-306.pdf
Size:
208.55 KB
Format:
Adobe Portable Document Format
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.86 KB
Format:
Item-specific license agreed to upon submission
Description:

Collections