Publication: Status Dystonicus with Atypical Presentation in Developmentally Delay Child: A Case Report
Date
2022
Journal Title
Journal ISSN
Volume Title
Publisher
Nepal Medical Association
Abstract
Abstract
Status dystonicus is characterised by involuntary sustained or intermittent muscle contractions of muscles causing repetitive twisting movements, abnormal postures of the body, or both is a rare but life-threatening movement disorder. Early diagnosis and management of status dystonicus prevent serious complications. We report a 2 years old previously developmental delay diagnosed girl who presented with generalised contractions of the whole body. Tightening of limbs is aggravated by touching her backside which is a very unique feature. Dystonia is associated with severe sweating and was confused with a seizure event. The patient was treated with midazolam, clonidine, phenytoin, gabapentin, pyridoxine, baclofen, and trihexyphenidyl. She was admitted to the intensive care unit for monitoring. The patient partially recovered after 10 days of treatment.
Description
Shailendra Kumar Yadav
Department of Pediatrics, Ishan Children and Women’s Hospital, Basundhara, Kathmandu, Nepal
https://orcid.org/0000-0001-6638-5503
Pratibha Yadav
Department of Pediatrics, The Second Affiliated Hospital of Kunming Medical University, Kunming, Yunnan, China
Gyabina Maharjan
Department of Pediatrics, Kirtipur Hospital, Kirtipur, Kathmandu, Nepal
Sujata Dahal
Department of Medicine, Patan Academy of Health Sciences, Lagankhel, Lalitpur, Nepal
Nirajan Khati
Department of Pediatrics, Vayodha Hospitals, Balkhu, Kathmandu, Nepal
Keywords
Aspiration, Children, Dystonia, Epilepsy, Pneumonia