Publication:
Joint Effusions And Purpura In Multiply-Transfused Adult Beta-Thalassemia- Clinical Pointers To Diagnosis Of Scurvy

creativeworkseries.issn1812-2027
dc.contributor.authorPrakash, A
dc.contributor.authorPandey, AK
dc.date.accessioned2025-09-08T07:33:01Z
dc.date.available2025-09-08T07:33:01Z
dc.date.issued2013
dc.descriptionPrakash A, Pandey AK Department of Medicine Lady Hardinge Medical College and Smt. Sucheta Kriplani Hospital, New Delhi, India
dc.description.abstractABSTRACT Periodic transfusions and effective chelation have ensured that thalassemics survive in to adulthood but their life is punctuated by peculiar problems in adulthood. Three cases of scurvy are being reported presenting uniquely as purpura, right hip joint effusion and right knee joint effusion with haemorrhage in prepatellar and retropatellar bursae, respectively over an 18 month period (2009-2010). The first two cases did give a history of gum bleed. None had any coagulation disturbance or transfusion-transmitted infections or connective tissue disorder. All the three cases responded dramatically to vitamin C supplementation. It is imperative to keep in mind that recurrent blood transfusions are associated with a state of sub- clinical vitamin C deficiency and overt scurvy may manifest as cumulative number of transfusions increase, as in adult thalassemics. KEYWORDS Joint effusion, scurvy, thalassemia, transfusion-dependent, ascorbic acid, vitamin C
dc.identifier.urihttps://hdl.handle.net/20.500.14572/2229
dc.language.isoen_US
dc.publisherKathmandu University
dc.titleJoint Effusions And Purpura In Multiply-Transfused Adult Beta-Thalassemia- Clinical Pointers To Diagnosis Of Scurvy
dc.typeArticle
dspace.entity.typePublication
local.article.typeShort Communication
oaire.citation.endPage362
oaire.citation.startPage360
relation.isJournalIssueOfPublication6ab4d6d7-4f65-42a5-86c5-ec2c619b0133
relation.isJournalIssueOfPublication.latestForDiscovery6ab4d6d7-4f65-42a5-86c5-ec2c619b0133
relation.isJournalOfPublicationa782b7ff-cf89-4178-ad1c-11ed89cfe1bd

Files

Original bundle
Now showing 1 - 1 of 1
Loading...
Thumbnail Image
Name:
360-362.pdf
Size:
461.48 KB
Format:
Adobe Portable Document Format
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.86 KB
Format:
Item-specific license agreed to upon submission
Description:

Collections