Article:
Late onset congenital cystic adenomatoid pulmonary malformation

creativeworkseries.issn1999-6217
dc.contributor.authorUrrea, Alejandro Rojas
dc.contributor.authorMariño, Daniela Arias
dc.contributor.authorVelandia, Duvan Felipe
dc.contributor.authorCalderon, Linette Marliece Olivares
dc.contributor.authorCoronel, Natalia Sanchez
dc.contributor.authorAgudelo, Lorena García
dc.creator.affiliationHealth Research Department, Hospital Regional de la Orinoquía
dc.creator.affiliationHealth Research Department, Hospital Regional de la Orinoquía
dc.creator.affiliationHealth Research Department, Hospital Regional de la Orinoquía
dc.creator.affiliationHealth Research Department, Hospital Regional de la Orinoquía
dc.creator.affiliationHealth Research Department, Hospital Regional de la Orinoquía
dc.creator.affiliationHealth Research Department, Hospital Regional de la Orinoquía
dc.date.accessioned2026-09-15T10:45:46Z
dc.date.available2026-09-15T10:45:46Z
dc.date.issued2025
dc.description.abstractAbstract: Congenital cystic adenomatoid pulmonary malformations are defined as the presence of a cystic mass of undifferentiated lung tissue; a third of the cases affect one of the lower lobes, and multilobar or bilateral affection is rare. The entity is a rare congenital malformation in the lungs, with an incidence of one in 11,000 to one in 35,000 live births. It is mainly discovered during the fetal period, although a low percentage of patients will be diagnosed postnatally. The disease has a wide spectrum of clinical manifestations, from asymptomatic to life-threatening respiratory symptoms. The diagnosis is made by imaging studies, and the treatment depends on the patient’s clinical status. We reported the case of an infant with a rare congenital pulmonary airway malformation and a late diagnosis, which makes the case even rarer, who required open lobectomy as treatment.
dc.identifier.doihttps://doi.org/10.33314/jnhrc.v23i02.4809
dc.identifier.urihttps://hdl.handle.net/20.500.14572/7707
dc.language.isoen_US
dc.publisherNepal Health Research Council
dc.subjectCongenital abnormalities
dc.subjectCystic adenomatoid malformation of lung
dc.subjectLung diseases
dc.titleLate onset congenital cystic adenomatoid pulmonary malformation
dc.typeArticle
dspace.entity.typePublication
local.article.typeCase Report
oaire.citation.endPage435
oaire.citation.startPage432
relation.isJournalIssueOfPublication5df7ea21-413e-4c7e-92f6-f85d6e7a64ef
relation.isJournalIssueOfPublication.latestForDiscovery5df7ea21-413e-4c7e-92f6-f85d6e7a64ef
relation.isJournalOfPublication40bd2739-8b19-447c-be60-723a1bdd1dcd

Files

Original bundle
Now showing 1 - 1 of 1
Loading...
Thumbnail Image
Name:
432-435.pdf
Size:
612.04 KB
Format:
Adobe Portable Document Format
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.86 KB
Format:
Item-specific license agreed to upon submission
Description:

Collections