Publication: Congenital Cystic Adenomatoid Malformation of the Lung: A Case Report
Date
2011
Authors
Article Type
Case Report
Journal Title
Journal ISSN
ISSN 1990-7974 eISSN 1990-7982
Volume Title
Pages
Pages: 64 - 67
Publisher
Nepal Paediatric Society (JNPS)
Abstract
Abstract:
Congenital cystic adenomatoid malformations (CCAM) of the lung are rare congenital cystic lung lesions that arise from excessive disorganized proliferation of tubular bronchial structures. The prenatal rate of detection of lung cysts at the routine 18–20-week scan is almost 100%.However as gestation progresses the tracheobronchial tree becomes patent and the fl uid within the cysts exits into the amniotic fl uid and the cysts collapse, allowing the other lobes of the lung to develop normally. Only at birth do the cysts then expand and present in the newborn period with respiratory distress. In late childhood or in adult life, it can present as recurrent chest infections or even undergo malignant transformation. We report a case of Type II CCAM in newborn with brief review of literature.
Description
M Sood
Registrar, Department of Paediatrics, IGMC, Shimla
Keywords
Cystic Adenomatoid Malformation
Identifier
https://doi.org/10.3126/jnps.v31i1.4162