Publication: A case of Hypomyopathic Dermatomyositis which subsequently developed to overt Myositis with ILD
Date
2022
Journal Title
Journal ISSN
Volume Title
Publisher
Nepalese Respiratory Society
Abstract
Abstract:
Dermatomyositis (DM) is an inflammatory myositis. Clinically amyopathic dermatomyositis (CADM) and hypomyopathic dermatomyositis (HDM) are rare forms of DM in which skin manifestations are present with no and minimal clinical and laboratory evidence of myositis respectively. A common complication of CADM/HDM is interstitial lung disease (ILD), with the most common histopathologic variant of non-specific interstitial pneumonia (NSIP). This case highlights the development of ILD and severe muscle weakness, including proximal limb muscles, muscles of respiration and muscles of deglutition in a patient with previous diagnosis of hypomyopathic dermatomyositis.
Description
Prayush Sharma
KIST Medical College and Teaching Hospital, Imadole
Abhijit Datta
Bangabandhu Sheikh Mujib Medical College Hospital, Faridpur, Bangladesh
Mohammed Zakir Hossain
Cumilla Medical College Hospital, Cumilla, Bangladesh
Keywords
Clinically Amyopathic Dermatomyositis (CADM), Dermatomyositis (DM), Hypomyopathic Dermatomyositis (HDM), Interstitial Lung Disease (ILD), Non-specific Interstitial Pneumonia