Publication:
Bruck Syndrome: A Rare Disorder in New-Born with Fractures and Contractures

creativeworkseries.issnISSN 1990-7974 eISSN 1990-7982
dc.contributor.authorDhaubhadel, Suraj
dc.contributor.authorBaniya, Bimala
dc.contributor.authorJoshi, Hema
dc.contributor.authorChapagain, Ram Hari
dc.contributor.authorPaudel, Krishna Prasad
dc.date.accessioned2026-01-23T01:55:53Z
dc.date.available2026-01-23T01:55:53Z
dc.date.issued2017
dc.descriptionSuraj Dhaubhadel National Academy of Medical Sciences (NAMS), Kanti Children's Hospital, Nepal Bimala Baniya National Academy of Medical Sciences (NAMS), Kanti Children’s Hospital Hema Joshi National Academy of Medical Sciences (NAMS), Kanti Children’s Hospital Ram Hari Chapagain National Academy of Medical Sciences (NAMS), Kanti Children’s Hospital Krishna Prasad Paudel National Academy of Medical Sciences (NAMS), Kanti Children’s Hospital
dc.description.abstractAbstract: Bruck syndrome is a very rare autosomal recessive syndrome consisting of bone fragility and congenital joint contractures. It is considered as a combination of arthrogryposis multiplex congenita and osteogenesis imperfecta, while some consider it as the autosomal recessive variant of osteogenesis imperfecta. According to the genotype, it has been classified into types 1 and 2. To our knowledge, only about 28 patients of this syndrome have been reported so far worldwide with none been reported from Nepal. Here, we present a patient with generalized osteopenia, bilateral femur fracture and congenital joint contractures of distal extremities.
dc.identifier.urihttps://hdl.handle.net/20.500.14572/4346
dc.language.isoen_US
dc.publisherNepal Paediatric Society (JNPS)
dc.subjectArthrogryposis
dc.subjectOsteogenesis imperfecta
dc.subjectBruck syndrome
dc.subjectNeonate
dc.subjectFKBP10 gene
dc.titleBruck Syndrome: A Rare Disorder in New-Born with Fractures and Contractures
dc.typeArticle
dspace.entity.typePublication
local.article.typeCase Report
oaire.citation.endPage279
oaire.citation.startPage276
relation.isJournalIssueOfPublication97340c14-0d1f-4808-806c-8504b2e33439
relation.isJournalIssueOfPublication.latestForDiscovery97340c14-0d1f-4808-806c-8504b2e33439
relation.isJournalOfPublication6f9be05c-05a9-4a3e-a5b5-a19a15ab042c

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