Publication: Non-necrotising Scleritis and Spherophakia in Marfan Syndrome: A Rare Situation Adhering to Hickam’s Dictum
Date
2025
Authors
Article Type
Case Report
Journal Title
Journal ISSN
1812-2027
Volume Title
Pages
Pages: 242 - 244
Publisher
Kathmandu University
Abstract
ABSTRACT
Marfan syndrome is an autosomal dominant, connective tissue disorder that
affects various systems of the body including the eyes. We present a case of
a 22 year old man with Marfan syndrome presented with a painful red left
eye. On examination he was diagnosed to have non-necrotising scleritis and
microspherophakia. Non-necrotising scleritis with microspherophakia is a
rare and arduous situation. This is an interesting case where Hickam’s dictum
prevails over its counter argument of Occam’s razor principle.
KEY WORDS
Marfan syndrome, Non-necrotising scleritis, Spherophakia
Description
Parajuli S,1 Sharma S,2 Shrestha R,1 Chapagain S,1
1Reiyukai Eiko Masunaga Eye Hospital
Banepa, Kavre, Nepal
2Mechi Eye Hospital
Birtamode, Jhapa, Nepal
Keywords
Marfan syndrome, Non-necrotising scleritis, Spherophakia