Publication: A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report
Date
2025
Journal Title
Journal ISSN
Volume Title
Publisher
Nepal Medical Association
Abstract
Abstract
Vein of Galen aneurysmal malformation is a rare intracranial arteriovenous malformation, coexistence with aortic arch anomalies is even more uncommon, carry high risk of morbidity and mortality related to endovascular procedure and poor neurological outcome. Vein of Galen aneurysmal malformation is a dilated venous pouch, a persistence of the embryonic median prosencephalic vein of Markowski. Often presents with high output cardiac failure, severe pulmonary hypertension, and systemic steal leading to hemodynamic compromise and multi organ failure. BicĂȘtre score scale determines the potential treatment option and prognosis of the disease. Aim of the medical treatment is initial stabilization of life threatening condition of severe heart failure followed by the definitive treatment with endovascular embolization. Treatment is a big challenge, specially if coexistence with aortic arch anomalies which increases the morbidity and mortality. We describe a term neonate found to have vein of Galen aneurysmal malformation associated with bovine aortic arch.
Description
Krishna Deo Mandal
Department of Pediatrics and Neonatology: Paropakar Maternity and Womenâs Hospital, Thapathali,Kathmandu, Nepal,
Kalpana Subedi
Department of Pediatrics and Neonatology: Paropakar Maternity and Womenâs Hospital, Thapathali,Kathmandu, Nepal,
Unnati Amatya
Obstetrics and Gynecology, Embassy of India, Kathmandu, Nepal
Janak Pathak
Department of Pediatrics and Neonatology: Paropakar Maternity and Womenâs Hospital, Thapathali,Kathmandu, Nepal,