Publication:
Generalised Epidermolysis Bullosa with Severe Anaemia in an Adolescent: A Case Report

creativeworkseries.issnISSN 1990-7974 eISSN 1990-7982
dc.contributor.authorJannawar, Shivam
dc.contributor.authorAmbike, Deepali
dc.contributor.authorAhmed, Sabahat
dc.contributor.authorKulkarni, Rajesh K
dc.contributor.authorAmbike, Deepali
dc.date.accessioned2025-12-11T09:43:10Z
dc.date.available2025-12-11T09:43:10Z
dc.date.issued2021
dc.descriptionShivam Jannawar Department of Paediatrics, Yashwantrao Chavan Memorial - Post Graduate Institute, Pune, India Deepali Ambike Department of Paediatrics, Yashwantrao Chavan Memorial - Post Graduate Institute, Pune, India Sabahat Ahmed Department of Paediatrics, Yashwantrao Chavan Memorial - Post Graduate Institute, Pune, India Rajesh K Kulkarni Department of Paediatrics, Yashwantrao Chavan Memorial - Post Graduate Institute, Pune, India Deepali Ambike YCM-PGI,Pune
dc.description.abstractAbstract: EBS is a rare genodermatosis usually inherited in an autosomal dominant fashion, although rare autosomal recessive cases have been reported. In severe generalised EBS, infants exhibit severe symptoms at the onset which tend to improve with time. We report an adolescent with severe generalised epidermolysis bullosa simplex (EBS), the most severe form of EBS, with severe iron deficiency anaemia.
dc.identifierhttps://doi.org/10.3126/jnps.v41i2.35059
dc.identifier.urihttps://hdl.handle.net/20.500.14572/3571
dc.language.isoen_US
dc.publisherNepal Paediatric Society (JNPS)
dc.subjectadolescent
dc.subjectGeneralised Epidermolysis Bullosa
dc.subjectsevere anaemia
dc.titleGeneralised Epidermolysis Bullosa with Severe Anaemia in an Adolescent: A Case Report
dc.typeArticle
dspace.entity.typePublication
local.article.typeCase Report
oaire.citation.endPage293
oaire.citation.startPage290
relation.isJournalIssueOfPublication70f2ee75-7114-4d4d-92c6-75b60827fd33
relation.isJournalIssueOfPublication.latestForDiscovery70f2ee75-7114-4d4d-92c6-75b60827fd33
relation.isJournalOfPublication6f9be05c-05a9-4a3e-a5b5-a19a15ab042c

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