Publication: Lewandowski & Lutz Syndrome: A Rare Case Entity
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Date
2017
Journal Title
Journal ISSN
Volume Title
Publisher
Society of Dermatologists, Venereologists and Leprologists of Nepal (SODVELON)
Abstract
Abstract:
Epidermodysplasia verruciformis (EV), first described in 1922 by Lewandowski and Lutz, is a rare inherited genetic disease. The disease usually manifests in childhood with highly polymorphic, widespread lesions.
We report a case of a fifteen year old boy, who presented to us with multiple flat topped, hypopigmented papules of a seven year duration on his body. He was diagnosed with EV on a skin biopsy, after ruling out differential diagnosis of pityriasis versicolor, verruca vulgaris and acrokeratosisverruciformis. The patient was resistant to known treatment options.
Key message: sun protection and lifelong observation for diagnosis and improved prognosis of malignant or premalignant lesions of EV.
Keywords: pityriasis versicolor, verruca-like lesions, sun exposed sites
Description
Rikta Mohan
Shri Ram Murti Smarak Institute of Medical Sciences
P Gahalaut
Shri Ram Murti Smarak Institute of Medical Sciences.
HS Soodan
Shri Ram Murti Smarak Institute of Medical Sciences.
N Mishra
Shri Ram Murti Smarak Institute of Medical Sciences.
MN Rastogi
Shri Ram Murti Smarak Institute of Medical Sciences.