Publication: Hypoplastic Left Heart Syndrome: A Case Report
| creativeworkseries.issn | JNMA Print ISSN: 0028-2715; Online ISSN: 1815-672X | |
| dc.contributor.author | Manandhar, Sunil Raja | |
| dc.contributor.author | Ghimire, Anjila | |
| dc.contributor.author | Rai, Dipendra | |
| dc.contributor.author | Shrestha, Sabina | |
| dc.contributor.author | Adhikari, Pritha | |
| dc.date.accessioned | 2025-08-28T05:40:09Z | |
| dc.date.available | 2025-08-28T05:40:09Z | |
| dc.date.issued | 2023 | |
| dc.description | Sunil Raja Manandhar Neonatology Unit, Department of Paediatrics, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal Anjila Ghimire Neonatology Unit, Department of Paediatrics, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal Dipendra Rai Neonatology Unit, Department of Paediatrics, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal 1. Sunil Raja Manandhar: drsunilraja@gmail.com Sabina Shrestha Neonatology Unit, Department of Paediatrics, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal Pritha Adhikari Neonatology Unit, Department of Paediatrics, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal | |
| dc.description.abstract | Abstract Hypoplastic left heart syndrome is a rare critical congenital heart defect constituting a prevalence of 1/3,500 to 1/12,500 live births in which there is obstructions to the blood flow within the left heart. Here we present a case of a full-term 38 weeks male baby with a birth weight of 3.5 kg, and no obvious physical deformity referred to our centre at 22 hours of life for respiratory distress and cyanosis. At 23 hours of life, he was diagnosed with hypoplastic left heart syndrome and kept on Prostaglandin E1 infusion till the 12th day of life. The baby had a large ventricular septal defect and atrial septal defect with a severely hypoplastic left ventricle, hypoplastic aortic root, ascending aorta and post-ductal coarctation of the aorta. The diagnosis was reconfirmed by computed tomography cardiac angiography on the 10th day of life with the same cardiac findings suggestive of hypoplastic left heart syndrome. | |
| dc.identifier | https://doi.org/10.31729/jnma.8243 | |
| dc.identifier.uri | https://hdl.handle.net/20.500.14572/2142 | |
| dc.language.iso | en_US | |
| dc.publisher | Nepal Medical Association | |
| dc.title | Hypoplastic Left Heart Syndrome: A Case Report | |
| dc.type | Other | |
| dspace.entity.type | Publication | |
| local.article.type | Case Report | |
| oaire.citation.endPage | 667 | |
| oaire.citation.startPage | 665 | |
| relation.isJournalIssueOfPublication | eb951073-19cf-4ca5-80ed-37fc7f0bb539 | |
| relation.isJournalIssueOfPublication.latestForDiscovery | eb951073-19cf-4ca5-80ed-37fc7f0bb539 | |
| relation.isJournalOfPublication | e6e146a0-0ece-4aba-aa0a-6ccfbd10a12a |