Publication: Holocord Syrinx, Tethered Cord and Diastematomyelia: Case Report and Review of Literature
Date
2012
Journal Title
Journal ISSN
Volume Title
Publisher
Nepal Paediatric Society (JNPS)
Abstract
Abstract:
Syringomyelia refers to the presence of cavities within the spinal cord or a dilatation of the central spinal cord canal. In 90% of cases, syringomyelia is associated with a Chiari I malformation. The association of syringomyelia with tethered cord is well known but syrinxes associated with these defects are usually below vertebral level T6. Holocord syrinx associated with tethered cord is rare and is almost always associated with Chiari 1 malformation. To the best of our knowledge, only a single case report of holocord syrinx with tethered cord has been reported, but this patient had multiple overt lumbosacral defects (tethered cord, meningocele and diastematomyelia). We are reporting a three year old child with holocord syrinx with tethered cord and diastematomyelia and no evidence of Chiari malformation, meningocele or any overt spinal malformation and minimal neurological abnormalities.
Description
A Maheshwari
Assistant Professor, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
D Yadav
Senior Resident, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
S Aneja
Director Professor, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
S Kaur
Senior Resident, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
B Patra
Senior Pediatrician, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
A Seth
Keywords
Tethered cord, Holocord syrinx, Diastematomyelia