Publication: Moyamoya Disease with Intraventricular Hemorrhage in a Child: A Case Report
Date
2025
Journal Title
Journal ISSN
Volume Title
Publisher
Institute of Medicine
Abstract
ABSTRACT
Moyamoya disease is a rare progressive cerebrovascular disorder in Nepal characterized by stenosis or occlusion of cerebral arteries with abnormal collateral vessels, and hemorrhagic presentation in children is extremely uncommon. We report an 8-year-old girl with intraventricular hemorrhage presenting with seizures, vomiting, and decreased consciousness. Imaging revealed characteristic angiographic features of Moyamoya disease. She was managed with external ventricular drainage and supportive treatment, achieving significant recovery. This case highlights the importance of considering Moyamoya disease in pediatric hemorrhagic stroke and underscores the need for early imaging and timely intervention.
Keywords: Moyamoya Disease; intraventricular hemorrhage; pediatric stroke
Description
Nisha Regmi1, Bibek Shrestha2, Vivek Karn3, Pradeep Raj Regmi4
¹College of Medical Sciences, Chitwan, Nepal
2Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal
3Department of Pediatrics, Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal
4Department of Radiology, Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal
Keywords
Moyamoya Disease, intraventricular hemorrhage, pediatric stroke