Article: Persistent Mullerian Duct Syndrome with Polysplenia and Short Pancreas: A Case Report
| creativeworkseries.issn | JNMA Print ISSN: 0028-2715; Online ISSN: 1815-672X | |
| dc.contributor.author | Sharma, Umesh Kumar | |
| dc.contributor.author | Thapa, Dinesh Kumar | |
| dc.contributor.author | Pokhrel, Dinesh | |
| dc.contributor.author | Shah, Amit Kumar | |
| dc.date.accessioned | 2026-08-31T07:06:22Z | |
| dc.date.available | 2026-08-31T07:06:22Z | |
| dc.date.issued | 2019 | |
| dc.description | Umesh Kumar Sharma Department of Radiology, B&C Medical College Teaching Hospital, Birtamod, Jhapa, Nepal Dinesh Kumar Thapa Department of Neurosurgery, B&C Medical College Teaching Hospital, Birtamod, Jhapa, Nepal Dinesh Pokhrel Department of Radiology, B&C Medical College Teaching Hospital, Birtamod, Jhapa, Nepal Amit Kumar Shah Department of Urology, B&C Medical College Teaching Hospital, Birtamod, Jhapa, Nepal | |
| dc.description.abstract | Abstract Persistent Mullerian duct syndrome is a rare entity and usually presents with common symptoms of undescended testis and hernia. The syndrome is caused by an insufficient amount of Mullerian inhibiting substance or due to the insensitivity of the target organ to Mullerian inhibiting substance. Polysplenia is a rare congenital disease manifested by multiple small accessory spleens. The association of these two entities is rare and has not been reported in the literature. We reported a case of a 27 years old male presented with complains of right flank pain and nausea. Ultrasound showed right ureteric calculus with hydronephrosis and elongated soft tissue mass posterior to bladder. Contrast enhanced Computed Tomography showed soft tissue suggestive of infantile uterine structure with multiple splenculi and short pancreas. He was diagnosed as Persistent Mullerian duct syndrome with unilateral cryptorchidism, polysplenia and short pancreas, coincidentally detected while evaluating for ureteric colic. Keywords: Persistent Mullerian duct syndrome; Polysplenia; Pancreas. | |
| dc.identifier | https://doi.org/10.31729/jnma.4298 | |
| dc.identifier.uri | https://hdl.handle.net/20.500.14572/7511 | |
| dc.language.iso | en_US | |
| dc.publisher | Nepal Medical Association | |
| dc.subject | Persistent Mullerian duct syndrome | |
| dc.subject | Polysplenia | |
| dc.subject | Pancreas | |
| dc.title | Persistent Mullerian Duct Syndrome with Polysplenia and Short Pancreas: A Case Report | |
| dc.type | Article | |
| dspace.entity.type | Publication | |
| local.article.type | Case Report | |
| oaire.citation.endPage | 126 | |
| oaire.citation.startPage | 123 | |
| relation.isJournalIssueOfPublication | 5274798b-8b38-4e42-b7fc-c3f3ecf86a1b | |
| relation.isJournalIssueOfPublication.latestForDiscovery | 5274798b-8b38-4e42-b7fc-c3f3ecf86a1b | |
| relation.isJournalOfPublication | e6e146a0-0ece-4aba-aa0a-6ccfbd10a12a |