Publication: Caffey Disease: A Diagnostic Dilemma
Date
2021
Journal Title
Journal ISSN
Volume Title
Publisher
Nepal Paediatric Society (JNPS)
Abstract
Abstract
Caffey disease is a rare, self limiting condition which usually presents in early infancy. The clinical features include fever, irritability, inflammatory swelling of soft tissue due to acute inflammation of the periosteum and subperiosteal new bone formation. Possible differential diagnoses are osteomyelitis, hypervitaminosis A, scurvy, bone tumours, prolonged use of Prostaglandin E1 (PGE1) and child abuse. Although self-limiting, it can cause diagnostic dilemma leading to delayed diagnosis and unnecessary investigations. Here, we report a case of two month old male infant presenting with painful left scapular mass.
Description
Shanti Regmi
Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Sudhir Adhikari
Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Deekshanta Sitaula
Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Ananda Prasad Regmi
Department of Orthopaedics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Gaurav Neupane
Department of Orthopaedics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Biraj Parajuli
Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Sumita Poudel
Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Keywords
Caffey Disease, Infantile Cortical Hyperpostosis, Osteomyelitis (CRMO)