Publication:
Caffey Disease: A Diagnostic Dilemma

Date

2021

Article Type

Case Report

Journal Title

Journal ISSN

ISSN 1990-7974 eISSN 1990-7982

Volume Title

Pages
Pages: 274 - 277

Publisher

Nepal Paediatric Society (JNPS)

Research Projects

Organizational Units

Journal Issue

Abstract

Abstract Caffey disease is a rare, self limiting condition which usually presents in early infancy. The clinical features include fever, irritability, inflammatory swelling of soft tissue due to acute inflammation of the periosteum and subperiosteal new bone formation. Possible differential diagnoses are osteomyelitis, hypervitaminosis A, scurvy, bone tumours, prolonged use of Prostaglandin E1 (PGE1) and child abuse. Although self-limiting, it can cause diagnostic dilemma leading to delayed diagnosis and unnecessary investigations. Here, we report a case of two month old male infant presenting with painful left scapular mass.

Description

Shanti Regmi Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Sudhir Adhikari Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Deekshanta Sitaula Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Ananda Prasad Regmi Department of Orthopaedics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Gaurav Neupane Department of Orthopaedics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Biraj Parajuli Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Sumita Poudel Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal

Keywords

Caffey Disease, Infantile Cortical Hyperpostosis, Osteomyelitis (CRMO)

Identifier

https://doi.org/10.3126/jnps.v41i2.34893

Citation

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