Article:
Caffey Disease: A Diagnostic Dilemma

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Abstract
Abstract Caffey disease is a rare, self limiting condition which usually presents in early infancy. The clinical features include fever, irritability, inflammatory swelling of soft tissue due to acute inflammation of the periosteum and subperiosteal new bone formation. Possible differential diagnoses are osteomyelitis, hypervitaminosis A, scurvy, bone tumours, prolonged use of Prostaglandin E1 (PGE1) and child abuse. Although self-limiting, it can cause diagnostic dilemma leading to delayed diagnosis and unnecessary investigations. Here, we report a case of two month old male infant presenting with painful left scapular mass.
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Shanti Regmi Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Sudhir Adhikari Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Deekshanta Sitaula Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Ananda Prasad Regmi Department of Orthopaedics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Gaurav Neupane Department of Orthopaedics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Biraj Parajuli Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal Sumita Poudel Department of Paediatrics, Chitwan Medical College, Bharatpur, Chitwan, Nepal
Keywords
Caffey Disease, Infantile Cortical Hyperpostosis, Osteomyelitis (CRMO)

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https://doi.org/10.3126/jnps.v41i2.34893

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