Publication:
Kartagener’s Syndrome: A Rare Case Authors

creativeworkseries.issnISSN 1990-7974 eISSN 1990-7982
dc.contributor.authorRicha
dc.contributor.authorPankaj Abrol
dc.contributor.authorShashi Sharma
dc.contributor.authorSakshee Madan
dc.date.accessioned2025-12-24T07:19:39Z
dc.date.available2025-12-24T07:19:39Z
dc.date.issued2020
dc.descriptionRicha Department of Paediatrics, SGT Medical College, Gurugram, Haryana, India Pankaj Abrol Department of Paediatrics, SGT Medical College, Gurugram, Haryana, India Shashi Sharma Department of Paediatrics, SGT Medical College, Gurugram, Haryana, India Sakshee Madan Department of Paediatrics, SGT Medical College, Gurugram, Haryana, India
dc.description.abstractAbstract: Kartagener’s syndrome, an autosomal recessively inherited disorder, is a subgroup of primary ciliary dyskinesias. This genetic disorder manifests from early life which distinguishes it from acquired mucociliary disorders. Kartagener’s syndrome presents as a classical triad of situs inversus, sinusitis and bronchiectasis occurring majorly due to impaired ciliary motility. Here we report a case of a four year old female child who presented to us with repeated episodes of cough and intermittent breathlessness for the past three years. Clinical examination revealed bilateral coarse basal crepitations and apex beat on right fifth intercostal space in the midclavicular line. A thorough investigation revealed situs inversus, chronic sinusitis, and bilateral bronchiectasis. The patient underwent a high-speed video microscopy analysis which was suggestive of primary ciliary dyskinesia. Considering these findings, the patient was diagnosed as a case of Kartagener’s syndrome.
dc.identifierhttps://doi.org/10.3126/jnps.v40i2.28845
dc.identifier.urihttps://hdl.handle.net/20.500.14572/3818
dc.language.isoen_US
dc.publisherNepal Paediatric Society (JNPS)
dc.subjectBronchiectasis
dc.subjectDynein
dc.subjectKartagener's syndrome
dc.subjectPrimary ciliary dyskinesia
dc.subjectSitus
dc.subjectinversus
dc.titleKartagener’s Syndrome: A Rare Case Authors
dc.typeArticle
dspace.entity.typePublication
local.article.typeCase Report
oaire.citation.endPage133
oaire.citation.startPage130
relation.isJournalIssueOfPublication2824c45f-d40b-4646-b754-b63604ec415f
relation.isJournalIssueOfPublication.latestForDiscovery2824c45f-d40b-4646-b754-b63604ec415f
relation.isJournalOfPublication6f9be05c-05a9-4a3e-a5b5-a19a15ab042c

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