Publication: Bulbar Onset Amyotrophic Lateral Sclerosis: A Case Report
Date
2023
Journal Title
Journal ISSN
Volume Title
Publisher
Nepal Medical Association
Abstract
Abstract
Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival.
Description
Kabindra Rai
KIST Medical College and Teaching Hospital, Mahalaxmi, Lalitpur, Nepal
Nilshan Rai
KIST Medical College and Teaching Hospital, Mahalaxmi, Lalitpur, Nepal
Milan Kumar Chhantel Thapa
KIST Medical College and Teaching Hospital, Mahalaxmi, Lalitpur, Nepal
Rajan Shrestha
KIST Medical College and Teaching Hospital, Mahalaxmi, Lalitpur, Nepal
Sampurna Singh
KIST Medical College and Teaching Hospital, Mahalaxmi, Lalitpur, Nepal
Monika Thapa
Department of Neurology, National Neuro Center, Maharajgunj, Kathmandu, Nepal
Keywords
amyotrophic lateral sclerosis, aspiration Pneumonia, Case reports, Edaravone