Publication: An Obstructed Malignant Inflammatory Myofibroblastic Tumour of the Rectum
Date
2018
Journal Title
Journal ISSN
Volume Title
Publisher
Kathmandu University
Abstract
ABSTRACT
Inflammatory myofibroblastic tumour is rare but more common in children. It
shows an immunophenotypic features of myofibroblastic differentiation, hence
bearing neoplastic potential. The diagnosis is challenging especially if it involves
rectum. Surgical resection is the mainstay of treatment if clinically obstructed.
A 65-year-old gentleman presented with intestinal obstruction, which then
followed by a hartmann’s procedure. Final diagnosis is a rare case of inflammatory
myofibroblastic tumour of the rectum. We discuss its genetic involvement with a
literature review.
KEY WORDS
Gastrointestinal tract, Myofibroblastic tumour, Rectum
Description
Zainal Abidin ZA,1 Azizan N,2 Hayati F,3 Mra A,3 Mohd Azman ZA4
1Department of General Surgery,
Surgical Sciences Cluster, Faculty of Medicine,
Universiti Teknologi MARA, Selangor, Malaysia.
2Department of Pathobiology and Medical Diagnostic,
Faculty of Medicine and Health,
Sciences, Universiti Malaysia Sabah, Sabah, Malaysia.
3Department of Surgery,
Faculty of Medicine and Health Sciences,
University Malaysia Sabah, Sabah, Malaysia.
4Department of Surgery,
Universiti Kebangsaan Malaysia,
Kuala Lumpur, Malaysia
Keywords
Gastrointestinal tract, Myofibroblastic tumour, Rectum