Publication: Rare Case of Servelle Martorelle Syndrome
Date
2012
Authors
Article Type
Case Report
Journal Title
Journal ISSN
1812-2027
Volume Title
Pages
Pages: 91 - 94
Publisher
Kathmandu University
Abstract
ABSTRACT
Servelle Martorelle Syndrome is a congenital vascular malformation associated with
soft tissue hypertrophy and bony hypoplasia. This rarely involves whole of an extremity,
with involvement of part of limbs reported in literature. We present a case of a twelve
year boy who presented to the Department of Plastic Surgery SGPGIMS in April 2011
,with history of circumferential soft tissue hypertrophy involving whole of left upper
limb, scapular region and axilla since birth. The entire left upper limb length was
lesser than the right upper limb. Hence this is a very rare case of Servelle Martorelle
Syndrome having extensive limb involvement at a very young age. Highlighted is the
role of conservative treatment and close follow-up to understand the natural history of
the diseases, with prompt treatment of complications.
KEY WORDS
Angio-osteohypotrophic angiodysplasia, venous malformation
Description
Bhatnagar A, Deshpande M
Dept of Plastic Surgery
SGPGIMS, Lucknow, India